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Dermatofibrosarcoma Protuberans of the Breast—a Rare Entity

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Abstract

Dermatofibrosarcoma protuberans (DFSP) represents about 1% of soft-tissue sarcomas with an estimated incidence of 0.8 to 5.0 cases per million per year. This lesion may occur anywhere in the body but more than 50% occur on the trunk, 20% on the head and neck and 30% on the extremities. DFSP of the breast is an extremely uncommon site of presentation. Data regarding DFSP of the breast is limited and mostly in the form of case reports. Clinical presentation is not uniform and may mimic benign skin lesions [1]. However, it typically presents as a nodular cutaneous mass in early or mid-adult life. We herein report a case of DFSP of the breast in a 33-year-old lady who was managed successfully in our institute and review the literature associated with it.

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Authors and Affiliations

  1. DNB Surgical Oncology, Chittaranjan National Cancer Institute, 37 SP Mukherjee Road, Kolkata, West Bengal, 700026, India

    Suvendu Maji

  2. Christian Medical College Vellore, Tamil Nadu, 632004, India

    MJ Paul

  3. Department Of Endocrine Surgery, Christian Medical College Vellore, Tamil Nadu, 632004, India

    Supriya Sen

Authors
  1. Suvendu Maji
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  2. MJ Paul
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  3. Supriya Sen
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Correspondence to Suvendu Maji.

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Maji, S., Paul, M. & Sen, S. Dermatofibrosarcoma Protuberans of the Breast—a Rare Entity. Indian J Surg Oncol 9, 351–354 (2018). https://doi.org/10.1007/s13193-017-0684-8

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  • DOI: https://doi.org/10.1007/s13193-017-0684-8

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